RESUMO
El cráneo en trébol es una malformación rara asociada al cierre temprano de múltiples suturas; se presenta con alteraciones en el desarrollo neurológico y una alta mortalidad. El tratamiento quirúrgico tiene como objetivo restaurar la forma y función del cráneo, en lo posible con el menor número de procedimientos.Este trabajo tiene como objetivo la presentación del caso de un lactante con deformidad de cráneo en trébol, caracterizado con el uso de ayudas diagnósticas e intervenido en un único tiempo quirúrgico con distracción de fosa posterior y remodelación de la bóveda craneal. (AU)
Cloverleaf skull is a rare malformation associated with early closure of multiple sutures; it presents with alterations in neurological development and high mortality. Surgical treatment aims to restore the shape and function of the skull, if possible with the fewest number of procedures.This paper aims to present the case of an infant with a cloverleaf skull deformity, characterized with the use of diagnostic aids and operated on in a single surgical stage with distraction of the posterior fossa and remodeling of the cranial vault. (AU)
Assuntos
Humanos , Masculino , Lactente , Crânio/anormalidades , Cabeça/anormalidades , Craniossinostoses/cirurgiaRESUMO
ABSTRACT: Acalvaria, also known as acrania, is a rare congenital anomaly which is characterized by a complete or partial defect of the calvarium. Due to the low number of patients reported, there is no a standard for the treatment of this condition; thereby, the objective is to present a new surviving patient with acalvaria and a novel surgical approach to treat it, giving craniofacial surgeons and neurosurgeons more tools to face it. In this article, the authors present a reproducible surgical approach in patients with partial acalvaria, which consist in use the present bone as a graft to cover the defect, giving a temporal but stable coverture. No other calvaria graft has been published along the available literature, since only around 4 patients are acalvaria survivors worldwide. However, the authors need to make a longer follow-up to establish the usefulness of the technique in long term. Other limitation is the future procedures needed to a better function and aesthetic.
Assuntos
Estética Dentária , Defeitos do Tubo Neural , Humanos , Crânio/cirurgiaRESUMO
Simple craniosynostosis is a cranial disease characterized by the premature closure of the cranial sutures, it develops during the first years of life and affects 1 in every 2000 to 2500 births worldwide (1). The cranial growth alteration occurs as parallel flattening to the compromised sutured with compensatory bulging in a perpendicular vector. Currently, The Suturectomy is the gold validated surgical treatment, that besides the dynamic Cranioplasties of multiples revolutions allows the design of bone flaps and therefore the correction of the secondary deformities caused by the synostosis. This multicenter descriptive study assessed a 20 series of cases (6 Plagiocephaly, 13 Scaphocephaly, 1 Brachycephaly) obtained in Cali, Colombia, that underwent surgery between January of 2014 and December of 2017, applying a Suturectomy surgery with additional telescoping of multiple revolution cranial osteotomies. The authors observe no clinical complications in the recruited patients regarding postoperative period of the described surgical technique (1, 90, and 180 days), thereby obtaining excellent outcomes on the maintained suture distraction focused on the assessment of the 3D reconstruction computed tomography scans.
